Fryns-Smeets-Thiry syndrome

ORPHA: 2058

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Fryns-Smeets-Thiry syndrome, sourced from HPO and Orphanet clinical annotations.

Wide mouthThick lower lip vermilionEverted lower lip vermilionMicrocephalyShort philtrumMicrognathiaProminent nasal bridgeNarrow nasal bridgeArachnodactylyIntellectual disabilityHypotoniaDisproportionate tall statureScoliosisDownturned corners of mouthHip dislocationShort statureCachexiaPatellar aplasiaJoint hypermobility

Classification & Codes

Orphanet Code

ORPHA:2058
Fryns-Smeets-Thiry syndrome
OrphanetORPHA:2058
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO