Fuchs' heterochromic uveitis

ORPHA: 263479

Overview

syndrome that is a chronic unilateral (or rarely bilateral) iridocyclitis appearing with the triad of heterochromia, predisposition to cataracts and glaucoma, and keratitic percipitates on the posterior corneal surface

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Fuchs' heterochromic uveitis, sourced from HPO and Orphanet clinical annotations.

Iris atrophyCorneal keratic precipitatesAnterior chamber inflammatory cellsVitreous floatersCataractBlurred visionHeterochromia iridisKoeppe nodulesBussaca nodulesGlaucomaPhotophobiaPapilledemaReduced visual acuityChorioretinal scarOcular hypertensionRed eyeAbnormal best corrected visual acuity testOcular painOptic disc pallorAnisocoriaRetinal perforationBest corrected visual acuity 0.1 LogMAREpiretinal membrane

Classification & Codes

Orphanet Code

ORPHA:263479
Fuchs' heterochromic uveitis
OrphanetORPHA:263479
Treatments0 drug(s)
Symptoms on record23 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO