gallbladder neuroendocrine neoplasm

ORPHA: 100086

Overview

neoplasm with neuroendocrine differentiation that arises from the gallbladder. It includes well differentiated neuroendocrine tumors (low and intermediate grade) and poorly differentiated neuroendocrine carcinomas (high grade)

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with gallbladder neuroendocrine neoplasm, sourced from HPO and Orphanet clinical annotations.

Biliary tract neoplasmNeuroendocrine neoplasmIntermittent jaundiceCholecystitisAscitesWeight lossNauseaAnorexiaEpisodic abdominal painChronic noninfectious lymphadenopathyAbdominal distentionBiliary tract obstructionElevated alkaline phosphatase of hepatic originExtrahepatic cholestasisChronic fatigueElevated gamma-glutamyltransferase levelNeoplasm of the nervous systemAbnormal brain FDG positron emission tomography

Classification & Codes

Orphanet Code

ORPHA:100086
gallbladder neuroendocrine neoplasm
OrphanetORPHA:100086
Treatments0 drug(s)
Symptoms on record18 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO