gamma chain deficiency

ICD-10: D80.0MeSH: D053632ORPHA: 276

Overview

immunodeficiency disorder in which the body produces very few T cells and NK cells

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with gamma chain deficiency, sourced from HPO and Orphanet clinical annotations.

Decreased CD4+ T cell proportionDecreased total lymphocyte countRecurrent feverPneumoniaAbnormal circulating immunoglobulin concentrationDecreased mitogen-induced T-cell proliferationDecreased naive T cell proportionReduced total natural killer cell countSkin rashDiarrheaRecurrent bacterial infectionsDecreased circulating IgA concentrationDecreased circulating IgG concentrationRecurrent opportunistic infectionsCoughAbnormally low T cell receptor excision circle levelDecreased total T cell countSepsisFailure to thriveChronic mucocutaneous candidiasisLymph node hypoplasiaRecurrent herpesRecurrent Haemophilus influenzae infectionsRecurrent bacterial skin infectionsSevere recurrent varicellaChronic oral candidiasisRecurrent cutaneous fungal infectionsAbsent tonsilsJaundiceHepatomegalyLymphomaIncreased circulating IgG concentrationLymphoproliferative disorder

Classification & Codes

ICD-10 Code

D80.0

MeSH Code

D053632

Orphanet Code

ORPHA:276
gamma chain deficiency
ICD-10D80.0
MeSHD053632
OrphanetORPHA:276
Treatments0 drug(s)
Symptoms on record33 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
gamma chain deficiency | OrphanDrug