generalized pustular psoriasis

ICD-10: L40.1ORPHA: 247353

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with generalized pustular psoriasis, sourced from HPO and Orphanet clinical annotations.

ArthralgiaElevated erythrocyte sedimentation rateErythematous plaquePustuleErythrodermaAbnormal nail morphologyPainArthritisFeverIncreased total leukocyte countElevated circulating C-reactive protein concentrationFatigueGeographic tongueOverweightCheilitisRenal insufficiencyObesityDecreased total lymphocyte countHypocalcemiaHyponatremiaElevated circulating hepatic transaminase concentrationHypoalbuminemiaPedal edemaPalmoplantar pustulosisUveitisCongestive heart failureSepsis

Classification & Codes

ICD-10 Code

L40.1

Orphanet Code

ORPHA:247353
generalized pustular psoriasis
ICD-10L40.1
OrphanetORPHA:247353
Treatments0 drug(s)
Symptoms on record27 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO