glycine encephalopathy

MeSH: D020158ORPHA: 407

Overview

amino acid metabolic disorder that involves abnormally high levels of the amino acid glycine in bodily fluids and tissues

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with glycine encephalopathy, sourced from HPO and Orphanet clinical annotations.

SeizureHypotoniaHypoplasia of the corpus callosumHyperglycinemiaEEG abnormalityEEG with burst suppressionAbnormal metabolic brain imaging by MRSRecurrent singultusLethargyPoor suckGeneralized myoclonic seizureBreathing dysregulationRespiratory acidosis

Classification & Codes

MeSH Code

D020158

Orphanet Code

ORPHA:407
glycine encephalopathy
MeSHD020158
OrphanetORPHA:407
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO