GRFoma

ORPHA: 97261

Overview

6cm and approximately 1/3 have metastasized at the time of diagnosis. It often co-occurs with Zollinger-Ellison syndrome or multiple endocrine neoplasia type 1 (MEN 1; see these terms).

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with GRFoma, sourced from HPO and Orphanet clinical annotations.

Elevated circulating growth hormone concentrationCoarse facial featuresAbnormal abdomen morphologyWeight lossDiarrheaNausea and vomitingConstipationAnorexiaZollinger-Ellison syndromeHepatomegalyEpisodic abdominal painNeoplasm of the pancreasIncreased circulating cortisol levelPoor appetitePalmoplantar hyperhidrosisHypoactive bowel soundsNeoplasm of the lungAbnormality of the thyroid glandIncreased circulating gonadotropin levelIncreased circulating prolactin concentrationSubcutaneous lipomaIntermittent jaundiceCholelithiasisIntrahepatic cholestasisAscitesGastrointestinal hemorrhagePituitary adenomaParathyroid adenomaHypercalcemiaIntestinal obstructionIntestinal carcinoidPrimary hyperparathyroidismAdrenocortical adenomaExtrahepatic cholestasisLack of bowel soundsNeoplasm of the small intestinePheochromocytomaNeoplasm of the thymus

Classification & Codes

Orphanet Code

ORPHA:97261
GRFoma
OrphanetORPHA:97261
Treatments0 drug(s)
Symptoms on record38 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO