Guadeloupean parkinsonism
ORPHA: 97355
Overview
Parkinsonism with dementia of Guadeloupe is characterised by symmetrical bradykinesia, predominantly axial rigidity, postural instability with early falls and cognitive decline with prominent features of frontal lobe dysfunction
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Guadeloupean parkinsonism, sourced from HPO and Orphanet clinical annotations.
ParkinsonismRigidityBradykinesiaVertical supranuclear gaze palsyHypometric saccadesDementiaFrontal lobe dementiaHallucinationsOrthostatic hypotensionDystoniaMyoclonusVentriculomegalyCerebral cortical atrophyPostural instabilityApraxiaPseudobulbar affectAction tremorSleep disturbanceEMG: myopathic abnormalitiesAutonomic bladder dysfunctionMidline brain calcificationsProgressive gait ataxiaWeakness due to upper motor neuron dysfunctionAbnormal autonomic nervous system physiologyT2 hypointense basal gangliaPalmomental reflex
Classification & Codes
Orphanet Code
ORPHA:97355Guadeloupean parkinsonism
| Orphanet | ORPHA:97355 |
| Treatments | 0 drug(s) |
| Symptoms on record | 26 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO