H syndrome

ORPHA: 168569

Overview

genetic condition

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with H syndrome, sourced from HPO and Orphanet clinical annotations.

AzoospermiaMicropenisAbnormality of the kidneyEnlarged kidneyHypogonadismCleft upper lipGingival overgrowthAmenorrheaHydrocephalusFull cheeksHearing impairmentProptosisAbnormal eyebrow morphologyGynecomastiaDiabetes mellitusDelayed pubertyHyperpigmentation of the skinIchthyosisHypertrichosisCorneal arcusMild intellectual disabilityHepatosplenomegalyAlopeciaPes planusHallux valgusMicrocytic anemiaRecurrent feverMalabsorptionBronchiectasisHypertriglyceridemiaChronic rhinitisVaricose veinsLymphadenopathyDelayed skeletal maturationRecurrent fracturesOsteolysisShort staturePsoriasiform dermatitisHyperreflexiaFacial telangiectasiaDecreased testicular sizeLipodystrophyAbnormal cardiovascular system physiologyCamptodactylyUpper eyelid edemaStiff skinSclerodermaHistiocytosisRecurrent pharyngitisHernia

Classification & Codes

Orphanet Code

ORPHA:168569
H syndrome
OrphanetORPHA:168569
Treatments0 drug(s)
Symptoms on record50 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO