Harel-Yoon syndrome

ORPHA: 496790

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Harel-Yoon syndrome, sourced from HPO and Orphanet clinical annotations.

Intellectual disabilityGlobal developmental delayAxial hypotoniaSpasticitySpastic gaitIncreased circulating lactate concentrationPoor speechPeripheral axonal neuropathyLower limb amyotrophyCryptorchidismLong faceMandibular prognathiaMicrognathiaHigh foreheadDeeply set eyeCataractMyopiaEsotropiaUpslanted palpebral fissureOptic nerve hypoplasiaNystagmusOptic atrophyPectus carinatumDelayed pubertyCerebellar atrophyHip dysplasiaHypertrophic cardiomyopathyGait ataxiaSleep disturbanceScoliosisShort nose3-Methylglutaconic aciduriaPositional foot deformityFeeding difficultiesSeizureCorneal opacity

Classification & Codes

Orphanet Code

ORPHA:496790
Harel-Yoon syndrome
OrphanetORPHA:496790
Treatments0 drug(s)
Symptoms on record36 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO