helicoid peripapillary chorioretinal degeneration

MeSH: C566236ORPHA: 86813

Overview

eye disease characterized by presence in the fundus of progressive bilateral retinal and choroidal atrophy leading to central vision loss that has material basis in heterozygous muation in TEAD1 on 11p15.3

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

MeSH Code

C566236

Orphanet Code

ORPHA:86813
helicoid peripapillary chorioretinal degeneration
MeSHC566236
OrphanetORPHA:86813
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO