hemidystonia-hemiatrophy syndrome

ORPHA: 306741

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hemidystonia-hemiatrophy syndrome, sourced from HPO and Orphanet clinical annotations.

HemiparesisDystoniaAbnormal periventricular white matter morphologyAbnormal basal ganglia MRI signal intensityAbnormal deliveryLimb dystoniaHemiatrophyAbnormal paranasal sinus morphologyDense calvariaSeizureBabinski signAbnormal pyramidal signAdvanced pneumatization of cranial sinusesMotor delayRhizomelic leg shortening

Classification & Codes

Orphanet Code

ORPHA:306741
hemidystonia-hemiatrophy syndrome
OrphanetORPHA:306741
Treatments0 drug(s)
Symptoms on record15 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO