hemoglobin E-beta-thalassemia syndrome

ORPHA: 2312492 Treatments Available

Available Treatments (2)

DrugFormStatusCountriesLead Time
luspatercept
Orphan Cold Chain
subcutaneous injection, 25 mg/vial, 75 mg/vial powder for solutionFDA Approved, EMA Approved810d
deferasirox
Orphan
oral tablet, 125 mg, 250 mg, 500 mg; oral granules for suspensionFDA Approved, EMA Approved105d

Clinical Presentation

Signs and symptoms associated with hemoglobin E-beta-thalassemia syndrome, sourced from HPO and Orphanet clinical annotations.

AnemiaImmunodeficiencyIncreased circulating ferritin concentrationAbnormal hemoglobin

Classification & Codes

Orphanet Code

ORPHA:231249
hemoglobin E-beta-thalassemia syndrome
OrphanetORPHA:231249
Treatments2 drug(s)
Symptoms on record4 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
hemoglobin E-beta-thalassemia syndrome | OrphanDrug