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hepatic veno-occlusive disease with immunodeficiency

ICD-10: K76.5ORPHA: 890

Contents

  1. 1. Available Treatments
  2. 2. Clinical Presentation
  3. 3. Classification & Codes

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hepatic veno-occlusive disease with immunodeficiency, sourced from HPO and Orphanet clinical annotations.

Renal insufficiencyJaundiceAscitesAbdominal painHepatomegalyRespiratory failureElevated circulating hepatic transaminase concentrationIncreased total bilirubinIncreased body weightAbnormality of coagulationProlonged partial thromboplastin timeHepatic encephalopathy

Classification & Codes

ICD-10 Code

K76.5

Orphanet Code

ORPHA:890
hepatic veno-occlusive disease with immunodeficiency
ICD-10K76.5
OrphanetORPHA:890
Treatments0 drug(s)
Symptoms on record12 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO