hereditary central diabetes insipidus
ICD-10: E23.2ORPHA: 30925
Overview
subtype of central diabetes insipidus (CDI, see this term) characterized by polyuria and polydipsia due to a genetically inherited decrease in vasopressin (AVP) production
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with hereditary central diabetes insipidus, sourced from HPO and Orphanet clinical annotations.
IrritabilityDiabetes insipidusLethargyGrowth delayWeight lossFeverPolydipsiaVomitingDiarrheaPolyuriaHyposthenuriaNocturia
Classification & Codes
ICD-10 Code
E23.2Orphanet Code
ORPHA:30925hereditary central diabetes insipidus
| ICD-10 | E23.2 |
| Orphanet | ORPHA:30925 |
| Treatments | 0 drug(s) |
| Symptoms on record | 12 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO