hereditary central diabetes insipidus

ICD-10: E23.2ORPHA: 30925

Overview

subtype of central diabetes insipidus (CDI, see this term) characterized by polyuria and polydipsia due to a genetically inherited decrease in vasopressin (AVP) production

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hereditary central diabetes insipidus, sourced from HPO and Orphanet clinical annotations.

IrritabilityDiabetes insipidusLethargyGrowth delayWeight lossFeverPolydipsiaVomitingDiarrheaPolyuriaHyposthenuriaNocturia

Classification & Codes

ICD-10 Code

E23.2

Orphanet Code

ORPHA:30925
hereditary central diabetes insipidus
ICD-10E23.2
OrphanetORPHA:30925
Treatments0 drug(s)
Symptoms on record12 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO