hereditary cystatin C amyloid angiopathy

ORPHA: 100008

Overview

a cerebral amyloid angiopathy that has material basis in an autosomal dominant mutation of CST3 on chromosome 20p11.21.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hereditary cystatin C amyloid angiopathy, sourced from HPO and Orphanet clinical annotations.

StrokeCerebral hemorrhageAmyloid depositionCerebral amyloid angiopathy

Classification & Codes

Orphanet Code

ORPHA:100008
hereditary cystatin C amyloid angiopathy
OrphanetORPHA:100008
Treatments0 drug(s)
Symptoms on record4 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO