hereditary lymphedema I

ORPHA: 79452

Overview

hereditary lymphedema characterized by autosomal dominant inheritance of chronic, generally painless, lower limb lymphedema with onset typically at birth or in early childhood

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hereditary lymphedema I, sourced from HPO and Orphanet clinical annotations.

LymphedemaHydrocele testisHyperkeratosisAnkle swellingVaricose veinsAbnormal venous morphologyPredominantly lower limb lymphedemaPedal edemaCellulitisToenail dysplasiaEpicanthusAtypical behaviorSpecific learning disabilityNeoplasm of the skinLichenificationAngiosarcomaErysipelasAbnormal facial shape

Classification & Codes

Orphanet Code

ORPHA:79452
hereditary lymphedema I
OrphanetORPHA:79452
Treatments0 drug(s)
Symptoms on record18 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO