hereditary pancreatitis
ORPHA: 676
Overview
congenital disorder of digestive system
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with hereditary pancreatitis, sourced from HPO and Orphanet clinical annotations.
Increased total leukocyte countAbdominal painElevated circulating C-reactive protein concentrationRecurrent pancreatitisAbnormal circulating enzyme concentration or activityDiabetes mellitusJaundicePancreatic calcificationSplanchnic vein thrombosis
Classification & Codes
Orphanet Code
ORPHA:676hereditary pancreatitis
| Orphanet | ORPHA:676 |
| Treatments | 0 drug(s) |
| Symptoms on record | 9 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO