hereditary sensory and autonomic neuropathy with spastic paraplegia

MeSH: C564948ORPHA: 139578

Overview

This syndrome is characterized by the association of an axonal sensory and autonomic neuropathy with spastic paraplegia

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hereditary sensory and autonomic neuropathy with spastic paraplegia, sourced from HPO and Orphanet clinical annotations.

Acral ulcerationSpasticitySpastic paraplegiaGait disturbanceHyperreflexiaDistal sensory impairment of all modalitiesImpaired pain sensationPeripheral neuropathyAbnormal autonomic nervous system physiologySkin ulcerAbnormal spinal cord morphologyClonusSensory axonal neuropathyDecreased motor nerve conduction velocityBabinski signDistal amyotrophyProgressive spastic paraplegiaFoot osteomyelitis

Classification & Codes

MeSH Code

C564948

Orphanet Code

ORPHA:139578
hereditary sensory and autonomic neuropathy with spastic paraplegia
MeSHC564948
OrphanetORPHA:139578
Treatments0 drug(s)
Symptoms on record18 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO