hereditary spastic paraplegia 10

MeSH: C537482ORPHA: 100991

Overview

hereditary spastic paraplegia that has material basis in mutation in the KIF5A gene on chromosome 12q13

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hereditary spastic paraplegia 10, sourced from HPO and Orphanet clinical annotations.

Pes cavusLower limb spasticityLower limb hyperreflexiaBabinski signSensorimotor neuropathyUpper limb amyotrophyModerate intellectual disabilityParkinsonismHearing impairmentRod-cone dystrophyDistal sensory impairmentPeripheral axonal neuropathyDistal lower limb amyotrophyCognitive impairmentSpastic paraparetic gaitAnkle clonusParesthesiaUpper limb spasticityScoliosisUpper motor neuron dysfunctionImpaired distal vibration sensationUpper limb hyperreflexiaUrinary urgencyVaricose veinsDupuytren contractureLeg muscle stiffnessLower limb muscle weaknessSpastic/hyperactive bladder

Classification & Codes

MeSH Code

C537482

Orphanet Code

ORPHA:100991
hereditary spastic paraplegia 10
MeSHC537482
OrphanetORPHA:100991
Treatments0 drug(s)
Symptoms on record28 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO