hereditary spastic paraplegia 31

MeSH: C565210ORPHA: 101011

Overview

30 years). In some cases, it can present as a complex phenotype with additional associated manifestations including peripheral neuropathy, bulbar palsy (with dysarthria and dysphagia), distal amyotrophy, and impaired distal vibration sense.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hereditary spastic paraplegia 31, sourced from HPO and Orphanet clinical annotations.

Gait disturbanceBrisk reflexesSpastic gaitProximal lower limb muscle weaknessHypertoniaPes cavusLower limb hyperreflexiaDistal sensory impairmentUpper limb hyperreflexiaProximal lower limb amyotrophyDifficulty runningImpaired proprioceptionDysarthriaSpastic tetraparesisDysphagiaBulbar signsHand muscle weakness

Classification & Codes

MeSH Code

C565210

Orphanet Code

ORPHA:101011
hereditary spastic paraplegia 31
MeSHC565210
OrphanetORPHA:101011
Treatments0 drug(s)
Symptoms on record17 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
hereditary spastic paraplegia 31 | OrphanDrug