hereditary spastic paraplegia 3A

MeSH: C536864ORPHA: 100984

Overview

hereditary spastic paraplegia that is characterized by lower limb weakness and spasticity that is generally non-progressive or extremely slow and has material basis in mutation in the ATL1 gene on chromosome 14q22

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hereditary spastic paraplegia 3A, sourced from HPO and Orphanet clinical annotations.

Lower limb spasticityLower limb hyperreflexiaBabinski signDistal lower limb muscle weaknessGait disturbanceSpastic gaitDistal lower limb amyotrophyAnkle clonusUrinary urgencyMotor delayImpaired vibratory sensationPeripheral neuropathyTip-toe gaitDysarthriaGrowth delayRigidityBradykinesiaFrequent fallsLower limb hypertoniaHyperesthesia

Classification & Codes

MeSH Code

C536864

Orphanet Code

ORPHA:100984
hereditary spastic paraplegia 3A
MeSHC536864
OrphanetORPHA:100984
Treatments0 drug(s)
Symptoms on record20 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO