Hirata disease
ORPHA: 411593
Overview
autoimmune disease of endocrine system characterized by hypoglycemia caused by antibodies to insulin
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Hirata disease, sourced from HPO and Orphanet clinical annotations.
Hyperinsulinemic hypoglycemiaInsulin-resistant diabetes mellitusInsulin resistanceSystemic lupus erythematosusIncreased circulating immunoglobulin concentrationAutoimmune antibody positivityAcanthosis nigricansWeight lossNonketotic hypoglycemiaAutoimmunityFasting hypoglycemiaArthralgia/arthritisReactive hypoglycemia
Classification & Codes
Orphanet Code
ORPHA:411593Hirata disease
| Orphanet | ORPHA:411593 |
| Treatments | 0 drug(s) |
| Symptoms on record | 13 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO