Hirata disease

ORPHA: 411593

Overview

autoimmune disease of endocrine system characterized by hypoglycemia caused by antibodies to insulin

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Hirata disease, sourced from HPO and Orphanet clinical annotations.

Hyperinsulinemic hypoglycemiaInsulin-resistant diabetes mellitusInsulin resistanceSystemic lupus erythematosusIncreased circulating immunoglobulin concentrationAutoimmune antibody positivityAcanthosis nigricansWeight lossNonketotic hypoglycemiaAutoimmunityFasting hypoglycemiaArthralgia/arthritisReactive hypoglycemia

Classification & Codes

Orphanet Code

ORPHA:411593
Hirata disease
OrphanetORPHA:411593
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO