holoprosencephaly-caudal dysgenesis syndrome

ORPHA: 2165

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with holoprosencephaly-caudal dysgenesis syndrome, sourced from HPO and Orphanet clinical annotations.

Abnormality of the genital systemRenal insufficiencyMedian cleft upper lipCleft palateMicrocephalyHypertelorismLow-set earsProptosisAbnormality of the skeletal systemHoloprosencephalyPremature birthAbnormal morphology of the radiusRadial ray deficiencyCyclopiaAbnormal diencephalon morphologyAbnormal cerebral vascular morphology

Classification & Codes

Orphanet Code

ORPHA:2165
holoprosencephaly-caudal dysgenesis syndrome
OrphanetORPHA:2165
Treatments0 drug(s)
Symptoms on record16 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
holoprosencephaly-caudal dysgenesis syndrome | OrphanDrug