Hughes-Stovin syndrome
ICD-10: M35.9ORPHA: 228116
Overview
disease
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Hughes-Stovin syndrome, sourced from HPO and Orphanet clinical annotations.
FeverNausea and vomitingPulmonary arterial hypertensionDyspneaHemoptysisPulmonary embolismHeadacheIncreased intracranial pressureVasculitisVenous thrombosisPulmonary artery aneurysmCardiorespiratory arrestPedal edemaFatigueCoughArterial stenosisAmaurosis fugaxChest pain
Classification & Codes
ICD-10 Code
M35.9Orphanet Code
ORPHA:228116Hughes-Stovin syndrome
| ICD-10 | M35.9 |
| Orphanet | ORPHA:228116 |
| Treatments | 0 drug(s) |
| Symptoms on record | 18 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO