Huntington disease-like 2

MeSH: C564708ORPHA: 98934

Overview

Huntington disease-like 2 (HDL2) is a severe neurodegenerative disorder considered part of the neuroacanthocytosis syndromes (see this term) characterized by a triad of movement, psychiatric, and cognitive abnormalities

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Huntington disease-like 2, sourced from HPO and Orphanet clinical annotations.

Personality changesAbnormality of movementAtypical behaviorDementiaGait disturbanceParkinsonismDystoniaHyperreflexiaWeight lossAbnormal cerebral morphologyChoreaCerebral cortical atrophyCaudate atrophyMemory impairmentPrimitive reflexFunctional motor deficitInvoluntary movementsAbnormal corpus striatum morphology

Classification & Codes

MeSH Code

C564708

Orphanet Code

ORPHA:98934
Huntington disease-like 2
MeSHC564708
OrphanetORPHA:98934
Treatments0 drug(s)
Symptoms on record18 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Huntington disease-like 2 | OrphanDrug