hydroa vacciniforme
ICD-10: L56.8MeSH: D006837ORPHA: 330058
Overview
rare skin disorder of unknown etiology affecting children
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with hydroa vacciniforme, sourced from HPO and Orphanet clinical annotations.
Cutaneous photosensitivityHydroa vacciniformeScarringMalar rashPapulovesicular eruptionKeratitisPhotophobiaEczematoid dermatitisHeadacheReduced visual acuityEpiphoraErythemaRed eyeSuperficial dermal perivascular inflammatory infiltrateLinear C3 deposits along the epidermal basement membrane zoneMalaiseTelangiectasia of the skin
Classification & Codes
ICD-10 Code
L56.8MeSH Code
D006837Orphanet Code
ORPHA:330058hydroa vacciniforme
| ICD-10 | L56.8 |
| MeSH | D006837 |
| Orphanet | ORPHA:330058 |
| Treatments | 0 drug(s) |
| Symptoms on record | 17 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO