hydrops-ectopic calcification-moth-eaten skeletal dysplasia

MeSH: C535858ORPHA: 1426

Overview

lethality and affected fetuses are considered as nonviable

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hydrops-ectopic calcification-moth-eaten skeletal dysplasia, sourced from HPO and Orphanet clinical annotations.

MicrognathiaNarrow chestPlatyspondylyLymphedemaBrachydactylyCalvarial skull defectAbnormal leukocyte morphologyMicromeliaAbnormal form of the vertebral bodiesDecreased skull ossificationAnterior rib punctate calcificationsSevere short-limb dwarfismRhizomeliaAbnormal pelvis bone ossificationMidface retrusionAbnormal bone ossificationAbnormally ossified vertebrae

Classification & Codes

MeSH Code

C535858

Orphanet Code

ORPHA:1426
hydrops-ectopic calcification-moth-eaten skeletal dysplasia
MeSHC535858
OrphanetORPHA:1426
Treatments0 drug(s)
Symptoms on record17 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO