hypochondroplasia

ICD-10: Q77.4MeSH: C562937ORPHA: 429

Overview

osteochondrodysplasia that has material basis in mutation in the FGFR3 gene which affects ossification of cartilage and results in short limb dwarfism

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hypochondroplasia, sourced from HPO and Orphanet clinical annotations.

MacrocephalyAbnormal metaphysis morphologyBrachydactylyIntellectual disabilityShort toeAbnormal pelvic girdle bone morphologyScoliosisSkeletal dysplasiaOsteoarthritisAbnormal femur morphologyGenu varumMicromeliaHyperlordosisAbnormal form of the vertebral bodiesSpinal canal stenosisBowing of the long bonesAbnormality of the elbowSleep apneaChildhood onset short-limb short statureJoint hypermobilityShort stature

Classification & Codes

ICD-10 Code

Q77.4

MeSH Code

C562937

Orphanet Code

ORPHA:429
hypochondroplasia
ICD-10Q77.4
MeSHC562937
OrphanetORPHA:429
Treatments0 drug(s)
Symptoms on record21 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
hypochondroplasia | OrphanDrug