hypomandibular faciocranial dysostosis

MeSH: C537154ORPHA: 1790

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hypomandibular faciocranial dysostosis, sourced from HPO and Orphanet clinical annotations.

Abnormal morphology of female internal genitaliaNarrow mouthCleft palateBifid uvulaTrigonocephalyBrachycephalyLow-set earsChoanal stenosisAnteverted naresDownslanted palpebral fissuresProptosisUpslanted palpebral fissureOptic disc colobomaCraniosynostosisPolyhydramniosAtrial septal defectPatent ductus arteriosusRecurrent respiratory infectionsTracheal stenosisShort noseMaxillozygomatic hypoplasiaAbnormal tracheobronchial morphologyLaryngeal hypoplasiaAplasia/Hypoplasia of the tongueMidface retrusionCognitive impairment

Classification & Codes

MeSH Code

C537154

Orphanet Code

ORPHA:1790
hypomandibular faciocranial dysostosis
MeSHC537154
OrphanetORPHA:1790
Treatments0 drug(s)
Symptoms on record26 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
hypomandibular faciocranial dysostosis | OrphanDrug