hypomyelinating leukodystrophy 5

MeSH: C567166ORPHA: 85163

Overview

Hypomyelination-congenital cataract is characterized by the onset of cataract either at birth or in the first two months of life, delayed psychomotor development by the end of the first year of life and moderate intellectual deficit

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hypomyelinating leukodystrophy 5, sourced from HPO and Orphanet clinical annotations.

Developmental cataractGlobal developmental delayAbnormal cerebellum morphologyModerate intellectual disabilityCerebral hypomyelinationAbnormal pyramidal sign

Classification & Codes

MeSH Code

C567166

Orphanet Code

ORPHA:85163
hypomyelinating leukodystrophy 5
MeSHC567166
OrphanetORPHA:85163
Treatments0 drug(s)
Symptoms on record6 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO