hypoparathyroidism, familial isolated

MeSH: C537156ORPHA: 2238

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hypoparathyroidism, familial isolated, sourced from HPO and Orphanet clinical annotations.

Cerebellar calcificationsHypoparathyroidismSeizureHypocalcemiaMyopathyAbnormal circulating calcium-phosphate regulating hormone concentrationCataractAbnormal dental enamel morphologyDelayed eruption of teethMuscle weaknessCerebral calcificationHyperphosphatemiaMuscle spasmHypocalcemic tetanyArrhythmiaNephropathyShort statureLaryngospasmGlobus pallidus calcification

Classification & Codes

MeSH Code

C537156

Orphanet Code

ORPHA:2238
hypoparathyroidism, familial isolated
MeSHC537156
OrphanetORPHA:2238
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
hypoparathyroidism, familial isolated | OrphanDrug