hypophosphatasia

MeSH: D007014ORPHA: 436

Overview

rare, and sometimes fatal, metabolic bone disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with hypophosphatasia, sourced from HPO and Orphanet clinical annotations.

Abnormality of the dentitionLarge fontanellesIrritabilityAbnormal rib morphologyNarrow chestAbnormal metaphysis morphologySkin dimple over apex of long bone angulationSeizureHypotoniaCraniosynostosisFailure to thrive in infancyAnemiaRespiratory insufficiencyEmphysemaRecurrent fracturesHypercalcemiaShort statureBowing of the long bonesFeeding difficulties in infancySkin dimple

Classification & Codes

MeSH Code

D007014

Orphanet Code

ORPHA:436
hypophosphatasia
MeSHD007014
OrphanetORPHA:436
Treatments0 drug(s)
Symptoms on record20 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO