ichthyosis bullosa of Siemens

MeSH: D053560ORPHA: 455

Overview

ia rare keratinopathic ichthyosis characterized by the presence of superficial blisters and erosions at birth

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with ichthyosis bullosa of Siemens, sourced from HPO and Orphanet clinical annotations.

Thin skinEdemaPalmoplantar keratodermaIchthyosisAbnormal blistering of the skinAcantholysisErythema

Classification & Codes

MeSH Code

D053560

Orphanet Code

ORPHA:455
ichthyosis bullosa of Siemens
MeSHD053560
OrphanetORPHA:455
Treatments0 drug(s)
Symptoms on record7 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO