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idiopathic and/or familial pulmonary arterial hypertension

ORPHA: 422

Contents

  1. 1. Available Treatments
  2. 2. Clinical Presentation
  3. 3. Classification & Codes

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with idiopathic and/or familial pulmonary arterial hypertension, sourced from HPO and Orphanet clinical annotations.

Pulmonary arterial hypertensionDyspneaAbnormal cardiovascular system physiologySyncopePalpitationsHepatomegalyRight ventricular dilatationTricuspid regurgitationFatigueHeart murmurElevated jugular venous pressureChest painPedal edema

Classification & Codes

Orphanet Code

ORPHA:422
idiopathic and/or familial pulmonary arterial hypertension
OrphanetORPHA:422
Treatments0 drug(s)
Symptoms on record13 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO