idiopathic pulmonary arterial hypertension

ORPHA: 275766

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with idiopathic pulmonary arterial hypertension, sourced from HPO and Orphanet clinical annotations.

DyspneaRight ventricular hypertrophyPulmonary arterial hypertensionElevated pulmonary artery pressureIncreased pulmonary vascular resistanceAbnormal jugular vein morphologySyncopeCongestive heart failureAnkle swellingTricuspid regurgitationEdema of the dorsum of feetHeart murmurChest painPalpitationsHemoptysisPedal edema

Classification & Codes

Orphanet Code

ORPHA:275766
idiopathic pulmonary arterial hypertension
OrphanetORPHA:275766
Treatments0 drug(s)
Symptoms on record16 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO