idiopathic pulmonary fibrosis
MeSH: D054990ORPHA: 2032
Overview
chronic, irreversible and ultimately fatal disease characterized by a progressive decline in lung function
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with idiopathic pulmonary fibrosis, sourced from HPO and Orphanet clinical annotations.
Abnormal pulmonary interstitial morphologyAcrocyanosisGastroesophageal refluxBronchiectasisPulmonary fibrosisExertional dyspneaFatigueCoughHoneycomb lungGround-glass opacificationReticular pattern on pulmonary HRCTCracklesSubpleural honeycombingUsual interstitial pneumoniaReduced forced vital capacityDecreased DLCOClubbing of fingersExercise intolerancePulmonic regurgitationOrthodeoxia
Classification & Codes
MeSH Code
D054990Orphanet Code
ORPHA:2032idiopathic pulmonary fibrosis
| MeSH | D054990 |
| Orphanet | ORPHA:2032 |
| Treatments | 0 drug(s) |
| Symptoms on record | 20 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO