IgG4-related hepatopathy

ORPHA: 90003

Overview

Inflammatory pseudotumor (IPT) of the liver is a rare benign tumor-like lesion

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with IgG4-related hepatopathy, sourced from HPO and Orphanet clinical annotations.

Neoplasm of the liverAbnormal liver sonographyFeverAbdominal painAutoimmune antibody positivityDiabetes mellitusBiliary tract abnormalityCirrhosisWeight lossVomitingNauseaAbdominal distentionAstheniaIncreased hepatitis B virus antibody levelElevated circulating aspartate aminotransferase concentrationElevated circulating alanine aminotransferase concentration

Classification & Codes

Orphanet Code

ORPHA:90003
IgG4-related hepatopathy
OrphanetORPHA:90003
Treatments0 drug(s)
Symptoms on record16 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO