IgG4-related hepatopathy
ORPHA: 90003
Overview
Inflammatory pseudotumor (IPT) of the liver is a rare benign tumor-like lesion
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with IgG4-related hepatopathy, sourced from HPO and Orphanet clinical annotations.
Neoplasm of the liverAbnormal liver sonographyFeverAbdominal painAutoimmune antibody positivityDiabetes mellitusBiliary tract abnormalityCirrhosisWeight lossVomitingNauseaAbdominal distentionAstheniaIncreased hepatitis B virus antibody levelElevated circulating aspartate aminotransferase concentrationElevated circulating alanine aminotransferase concentration
Classification & Codes
Orphanet Code
ORPHA:90003IgG4-related hepatopathy
| Orphanet | ORPHA:90003 |
| Treatments | 0 drug(s) |
| Symptoms on record | 16 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO