ileal neuroendocrine tumor, well differentiated, low or intermediate grade
ORPHA: 100078
Overview
well differentiated, low or intermediate grade tumor with neuroendocrine differentiation that arises from the ileum
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with ileal neuroendocrine tumor, well differentiated, low or intermediate grade, sourced from HPO and Orphanet clinical annotations.
Small intestine carcinoidDermatological manifestations of systemic disordersIntermittent diarrheaEpisodic abdominal painIncreased serum serotoninWeight lossIron deficiency anemiaNauseaEpisodic vomitingLymphadenopathyElevated circulating hepatic transaminase concentrationElevated serum acid phosphataseGastrointestinal obstructionFunctional intestinal obstructionExtrahepatic cholestasisChronic fatigueArterial occlusionAbnormal bowel soundsIntestinal fistulaHydronephrosisEdemaHepatic failurePulmonic stenosisRight ventricular failurePalpitationsZollinger-Ellison syndromeHypotensionTricuspid stenosisArrhythmiaAbnormal bronchus morphologyCardiogenic shock
Classification & Codes
Orphanet Code
ORPHA:100078ileal neuroendocrine tumor, well differentiated, low or intermediate grade
| Orphanet | ORPHA:100078 |
| Treatments | 0 drug(s) |
| Symptoms on record | 31 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO