inclusion body myositis

MeSH: D018979ORPHA: 611

Overview

inflammatory muscle disease in older adults

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with inclusion body myositis, sourced from HPO and Orphanet clinical annotations.

AutoimmunityRagged-red muscle fibersSkeletal muscle atrophyElevated circulating creatine kinase concentrationEMG abnormalityProximal muscle weaknessQuadriceps muscle weaknessRimmed vacuolesAbnormal muscle fiber morphologyInflammatory myopathyReduced tendon reflexesFeeding difficulties in infancyAnti-cytosolic-5-nucleotidase-1A antibody positivityMyalgia

Classification & Codes

MeSH Code

D018979

Orphanet Code

ORPHA:611
inclusion body myositis
MeSHD018979
OrphanetORPHA:611
Treatments0 drug(s)
Symptoms on record14 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO