OrphanDrug
OrphanDrug
Pharma Knowledge Base

indolent systemic mastocytosis

ICD-10: D47.0ORPHA: 98848

Contents

  1. 1. Overview
  2. 2. Available Treatments
  3. 3. Clinical Presentation
  4. 4. Classification & Codes

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with indolent systemic mastocytosis, sourced from HPO and Orphanet clinical annotations.

Abnormal bone marrow cell morphologyAbnormal skin morphologyIncreased proportion of CD25+ mast cellsAbnormal mast cell morphologyMastocytosisOsteoporosisSkin rashPruritusUrticariaGeneralized abnormality of skinAllergyDarier's signFlushingElevated total serum tryptaseAbdominal crampsMaculopapular exanthemaAnaphylactic shockSplenomegalyHepatomegalyLymphadenopathy

Classification & Codes

ICD-10 Code

D47.0

Orphanet Code

ORPHA:98848
indolent systemic mastocytosis
ICD-10D47.0
OrphanetORPHA:98848
Treatments0 drug(s)
Symptoms on record20 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO