Insulin-resistance syndrome type B
ORPHA: 2298
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Insulin-resistance syndrome type B, sourced from HPO and Orphanet clinical annotations.
HyperinsulinemiaInsulin resistanceAcanthosis nigricansWeight lossGlucose intoleranceSystemic lupus erythematosusAutoimmunityHyperglycemiaElevated erythrocyte sedimentation rateAbnormal circulating fatty-acid concentrationAbnormal oral glucose toleranceFasting hyperinsulinemiaPostprandial hyperglycemiaHypotriglyceridemiaProteinuriaNephritisPolycystic ovariesInsulin-resistant diabetes mellitusHirsutismDecreased total leukocyte countHypoalbuminemiaGlycosuriaAbnormal circulating lipid concentrationAntinuclear antibody positivityAbnormality of body weightDecreased body weightAbnormal circulating leptin concentrationDecreased circulating complement factor B concentrationType II diabetes mellitusEnlarged polycystic ovariesFatigueIncreased serum testosterone levelEnlarged ovariesHyperinsulinemic hypoglycemiaSkin rashAlopeciaThrombocytopeniaKetosisDiabetic ketoacidosisPneumoniaBiliary cirrhosisLymphomaOsteoarthritisFasting hypoglycemiaIncreased circulating IgG concentrationIncreased circulating IgA concentrationIncreased body weightMultiple myelomaAbnormal salivary gland morphologyHodgkin lymphoma
Classification & Codes
Orphanet Code
ORPHA:2298Insulin-resistance syndrome type B
| Orphanet | ORPHA:2298 |
| Treatments | 0 drug(s) |
| Symptoms on record | 50 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO