intellectual disability-severe speech delay-mild dysmorphism syndrome

ORPHA: 391372

Available Treatments (0)

No treatments linked yet

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Clinical Presentation

Signs and symptoms associated with intellectual disability-severe speech delay-mild dysmorphism syndrome, sourced from HPO and Orphanet clinical annotations.

Delayed speech and language developmentExpressive language delaySpeech articulation difficultiesProminent foreheadAbnormality of the genitourinary systemOpen mouthMandibular prognathiaHypertelorismRecurrent otitis mediaBroad nasal tipAbnormality of the eyeStrabismusDownslanted palpebral fissuresPtosisAbnormality of refractionAtypical behaviorAutistic behaviorShort attention spanAnxietySingle transverse palmar creaseSpasticityMotor delayFlexion contractureFailure to thriveAbnormal heart morphologyConstipationFrontal upsweep of hairModerate intellectual disabilityDownturned corners of mouthRecurrent upper respiratory tract infectionsShort noseProminent nasolabial foldOromotor apraxiaRepetitive compulsive behaviorSevere intellectual disabilityChin with horizontal creaseFeeding difficultiesThick vermilion borderBrain imaging abnormalityAbnormality of the kidneyMacrocephalyRetrognathiaBlepharophimosisAbnormality of the earNystagmusDiabetes mellitusHypothyroidismProminent fingertip padsSeizureHypotoniaMild intellectual disabilityRecurrent skin infectionsPulmonary arterial hypertensionEEG abnormalityAttention deficit hyperactivity disorderHypoplastic helicesAllergyOverweightClinodactylyDecreased circulating iron concentration

Classification & Codes

Orphanet Code

ORPHA:391372
intellectual disability-severe speech delay-mild dysmorphism syndrome
OrphanetORPHA:391372
Treatments0 drug(s)
Symptoms on record60 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO