intestinal dysganglionosis

ICD-10: Q43.1MeSH: C537394ORPHA: 998112 Treatments Available

Overview

Human disease

Available Treatments (2)

DrugFormStatusCountriesLead Time
Total Parenteral Nutrition
Cold Chain
IV infusion, customized formulationsFDA Approved115d
Erythromycin
Oral tablets 250mg, 500mg; IV infusion; Oral suspension 200mg/5mLFDA Approved82d

Clinical Presentation

Signs and symptoms associated with intestinal dysganglionosis, sourced from HPO and Orphanet clinical annotations.

Natal toothPatent ductus arteriosusMalabsorptionRecurrent infectionsDecreased circulating immunoglobulin concentrationCongenital diaphragmatic herniaAbnormal cardiac septum morphology

Classification & Codes

ICD-10 Code

Q43.1

MeSH Code

C537394

Orphanet Code

ORPHA:99811
intestinal dysganglionosis
ICD-10Q43.1
MeSHC537394
OrphanetORPHA:99811
Treatments2 drug(s)
Symptoms on record7 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO