isolated lissencephaly type 1 without known genetic defects

ORPHA: 1084

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with isolated lissencephaly type 1 without known genetic defects, sourced from HPO and Orphanet clinical annotations.

SeizureSpasticityPachygyriaNeonatal hypotoniaVentriculomegalyProfound intellectual disabilityGray matter heterotopiaHypsarrhythmiaAxial hypotoniaSevere intellectual disabilityEEG with changes in voltageFeeding difficultiesInfantile spasmsNeurodevelopmental delayMotor seizureAgyriaEnlarged sylvian cistern

Classification & Codes

Orphanet Code

ORPHA:1084
isolated lissencephaly type 1 without known genetic defects
OrphanetORPHA:1084
Treatments0 drug(s)
Symptoms on record17 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO