isolated trigonocephaly
ORPHA: 3366
Overview
Isolated trigonocephaly is a nonsyndromic form of craniosynostosis characterized by the premature fusion of the metopic suture
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with isolated trigonocephaly, sourced from HPO and Orphanet clinical annotations.
TrigonocephalyMetopic synostosisProminent supraorbital ridgesNarrow foreheadWide nasal bridgeHypotelorismSynophrysHighly arched eyebrowDelayed speech and language developmentOmphalocelePapilledemaIncreased intracranial pressure
Classification & Codes
Orphanet Code
ORPHA:3366isolated trigonocephaly
| Orphanet | ORPHA:3366 |
| Treatments | 0 drug(s) |
| Symptoms on record | 12 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO