juvenile neuronal ceroid lipofuscinosis

ICD-10: E75.4ORPHA: 98544

Overview

extremely rare and fatal autosomal recessive neurodegenerative disorder in humans

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

ICD-10 Code

E75.4

Orphanet Code

ORPHA:98544
juvenile neuronal ceroid lipofuscinosis
ICD-10E75.4
OrphanetORPHA:98544
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
juvenile neuronal ceroid lipofuscinosis | OrphanDrug