Kallmann syndrome-heart disease syndrome

ORPHA: 2326

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Kallmann syndrome-heart disease syndrome, sourced from HPO and Orphanet clinical annotations.

Hypogonadotropic hypogonadismIntellectual disabilityTotal anosmiaMicropenisRenal agenesisCleft palateShort lingual frenulumSensorineural hearing impairmentDelayed pubertyOsteopeniaOsteoporosisCyanosisGrowth delayDilated cardiomyopathyDouble outlet right ventricleDelayed skeletal maturationShort staturePulmonary artery hypoplasiaBilateral cryptorchidismDecreased testicular sizePartial anosmiaAnomalous origin of left coronary artery from the pulmonary arteryRight aortic archHeart murmurCongestive heart failureMitral regurgitationAortic regurgitationMidgut malrotationPulmonic regurgitation

Classification & Codes

Orphanet Code

ORPHA:2326
Kallmann syndrome-heart disease syndrome
OrphanetORPHA:2326
Treatments0 drug(s)
Symptoms on record29 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO