kaposiform hemangioendothelioma

MeSH: C537007ORPHA: 2122

Contents

1. Overview
2. Available Treatments
3. Clinical Presentation
4. Classification & Codes

Overview

Kaposiform hemangioendothelioma is a very rare, aggressive, vascular tumor manifesting in the neonatal period or in infancy as cutaneous vascular tumors to large infiltrative lesions

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with kaposiform hemangioendothelioma, sourced from HPO and Orphanet clinical annotations.

Chronic disseminated intravascular coagulationHypofibrinogenemiaPainErythematous plaqueErythematous papuleElevated circulating D-dimer concentrationHyperhidrosisPetechiaeEdemaPurpuraLymphedemaThrombocytopeniaMicroangiopathic hemolytic anemiaHypertrichosis

Classification & Codes

MeSH Code

C537007

Orphanet Code

ORPHA:2122

kaposiform hemangioendothelioma

MeSH	`C537007`
Orphanet	`ORPHA:2122`
Treatments	0 drug(s)
Symptoms on record	14 signs
Status	published

Factual Authority

Last Updated3/20/2026

Clinical DataHPO · Orphanet

Drug DataFDA · EMA · CDSCO