Kasabach-Merritt syndrome

ICD-10: D69.5MeSH: D059885ORPHA: 3325

Overview

rare disease usually seen in infants

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Kasabach-Merritt syndrome, sourced from HPO and Orphanet clinical annotations.

ThromboembolismAutoimmune thrombocytopeniaHypercoagulabilityDeep venous thrombosisIncreased serum serotoninArterial thrombosisVenous thrombosisStrokeMyocardial infarctionPulmonary embolismCerebral ischemiaDisseminated intravascular coagulationIncreased inflammatory responseMesenteric venous thrombosisAbnormal onset of bleeding

Classification & Codes

ICD-10 Code

D69.5

MeSH Code

D059885

Orphanet Code

ORPHA:3325
Kasabach-Merritt syndrome
ICD-10D69.5
MeSHD059885
OrphanetORPHA:3325
Treatments0 drug(s)
Symptoms on record15 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO